豆

Objective To improve the MRI diagnostic accuracy and the understanding of hepatolenticular degeneration by analyzing the magnetic rescnance imaging features.

内容摘要：［摘要］目的：分析肝豆状核变性的颅脑MRI征象，进一步提高对HLD病的认识及诊断的正确率。

MRI is one of the most efficient methods in diagnosis of hepatolenticular degeneration.Its signal changes can assess progress of disease,curative efficacy and prognosis.

MRI是诊断肝豆状核变性最有效方法之，其信号变化可反映病程并判断疗效及预后。

MRI is one of the most efficient methods in diagnosis of hepatolenticular degeneration.Its signal changes can assess progress of disease,curative efficacy and prognosis.

MRI是诊断肝豆状核变性最有效方法之一，其信号变化可反映病程并判断疗效及预后。

OBJECTIVE: To establish a hepatolenticular degeneration rat model with excessive copper, and investigate the effects of excessive copper deposits in the liver on hepatocyte apoptosis and Bax and Bcl-2 expression.

目的：建立肝豆状核变性铜过量负荷大鼠模型，并研究肝铜沉积对肝细胞凋亡及Bax，Bcl-2基因表达的影响。

Clinical analysis of 45 cases with hepatolenticular degeneration.

褚波，杜捷夫，孟庆义。45例肝豆状核变性的临床分析。

To investigate the relationship between Arg778Leu mutation of ATPTB gene and clinical manifestation in hepatolenticular degeneration.

目的：探讨肝豆状核变性（Hepatolenticular Degeneration，HLD）患者ATP7B基因Arg778Leu突变型与临床表现之间的相关性。

Methods The clinical data of splenectomy for the treatment of children with hepatolenticular degeneration complicated with hypersplenism were analyzed retrospectively. The comparison was made on the changes of blood cell and pre- and post-opertive immunoglobulin.

回顾分析30例小儿肝豆状核变性合并脾功能亢进而行脾切除的临床资料，对手术前后血细胞和免疫球蛋白的变化进行比较。

Objective To summarize the long-term effect of combined treatment with large-dose zinc sulfate and low-dose penicillamine in children with hepatolenticular degeneration.

目的 总结大剂量硫酸锌与小剂量青霉胺联合治疗儿童肝豆状核变性(hepatolenticular degeneration，HLD)的远期效果。

Splenectomy is valuable in treating children with hepatolenticular degeneration complicated with hypersplenism.

脾切除是小儿肝豆状核变性合并脾功能亢进的主要治疗措施，它能保证患儿继续驱铜治疗。

Hepatolenticular Degeneration , also called Wilson's Disease is an autosomal recessive inherited disease, which mainly affects children and adolescents.

肝豆状核变性（Hepatolenticular Degeneration，HLD）又称Wilson's病，是一种好发于青少年的常染色体隐性遗传病。

The split between the two groups can hardly be papered over.

这两个团体间的分歧难以掩饰。

This approach not only encourages a greater number of responses, but minimizes the likelihood of stale groupthink.

这种做法不仅鼓励了更多的反应，而且减少跟风的可能性。