血管瘤病

Results (1) 6 cases of Tuberous Sclerosis. Diffused subependymal nodular calcification lesions were found in all cases on unenhenced CT. 4 patients are 2 pairs of mother/child relationship. Both of the two mothers are found to suffer from renal angiomyolipoma.(2)1 case of neurofibromatosis showed abnormal spinal canal: scoliosis of thoracic and lumbar spine, concave change of vertebral posterior border. Bilateral renal hypogenesis was found in this patient. Diffused hyper-density lesions were found in kidney and fatty accumulation was found in back skin.(3)6 cases of Sturge-Weber syndrome. On unenhenced CT, curving and strip-shaped calcifications were found along the parietal and occipital gyrus.

结果 ①结节性硬化6例，所有病例CT平扫见两侧脑室室管膜下多发小结节状高密度钙化灶，其中4例为两对母子关系，并见两位母亲合并有肾脏错构瘤，；②神经纤维瘤病1例，MRI表现为椎管异常，胸腰段脊柱侧弯，椎体后缘呈明显的切凹改变；伴有双肾发育不良，CT示肾内多个高密度影，背部皮肤多量脂肪堆积，③脑颜面血管瘤综合征6例， CT可见顶枕部沿脑回分布的弯曲的条状高密度钙化，部分延伸致侧脑室内，增强后见病灶内有扭曲的条状和结节状明显强化的血管影；④小脑血管瘤病4例，影像学表现为小脑内大囊、小结节样占位性病变。

Combined with typical clinical symptoms and signs,MRI can make an accurate diagnosis to encephalofacial angiomatosis.

结合典型的临床症状和体征，MRI可以对脑颜面血管瘤病做出比较明确的诊断。

Abstract］ Objective To explore the diagnostic value of MRI in encephalofacial angiomatosis. Methods The MRI findings were retrospectively studied in 5 cases of encephalofacial angiomatosis proved by histological examinations,its MRI data, clinical performance and pathogenesis were summarized and analysed.

目的 探讨磁共振成像对脑颜面血管瘤病的诊断价值方法收集5例经临床和手术证实的脑颜面血管瘤病，对其磁共振资料、临床表现和发病机制进行回顾性的总结和分析。

In 14 patients with angiogenic tumors of the soft tissue ( 13 benign tumors and 1 malignant tumor) were analyzed. Results Benign hemangiomas included cavernous (n=7), intramuscular (n=2), mixed (n=1), racemosum (n=1), glomus (n=1) and angiomatosis (n=1). The vascular component within the tumor displayed iso-intensity on T1WI relative to the skeletal muscle, and hyper-intensity on T2WI. One case of hemangiopericytoma showed slightly low signal on T1WI and slightly high signal on T2WI.

结果 13例良性肿瘤中，海绵状血管瘤7例，肌肉内血管瘤2例，混合型血管瘤、蔓状血管瘤、血管球瘤、血管瘤病各1例，瘤血管成分在T1WI上呈等信号，T2WI上呈高信号，肿瘤有不等量的纤维组织和脂肪组织；血管外皮细胞瘤1例，T1WI上呈略低信号，T2WI上呈略高信号。

SWS, also known as encephalotrigeminal angiomatosis or meningiofacial angiomatosis, is a rare neurocutaneous syndrome that includes a facial port wine stain and associated leptomeningeal angiomatosis.

SWS，又被称为脑颜面神经血管瘤病或脑三叉神经血管瘤病，是一种少见的神经皮肤综合症，包括颜面部葡萄酒色素痣和软脑膜血管瘤病。

Babies may develop a type of hepatic hemangioma called benign infantile hemangioendothelioma (also called multinodular hepatic hemangiomatosis).

宝宝可能发展一种叫婴儿良性血管内皮细胞瘤肝血管瘤(又称多结节性肝血管瘤病)。

Meningioangiomatosis is a rare, benign, hamartomatous lesion involving the cerebral cortex and leptomeninges.

脑膜血管瘤病是一种少见、良性的错构瘤，主要累及皮质及软脑膜。

She is especially good at the management of the eyeground diseases, such as ocular fundus bleeding from various reasons, retinal vascular diseases (such as diabetic retinopathy, retinal vein occlusion, retinal artery occlusion, retinal vasculitis etc.) from diabetes mellitus, hypertension, or various inflammation, retinal capillary hemangioma, vitreous hemorrhage caused by various retinal diseases, optic neuritis, ischemic optic neuropathy, retinal detachment, macular diseases (such as age related macular degeneration, central serous chorioretinopathy, central exudative chorioretinopathy etc.), and other complex diseases such as uveitic diseases and glaucoma etc.

特别是对眼底病如各种原因所致眼底出血；糖尿病、高血压、各种炎症所引起的视网膜血管病如糖尿病视网膜病变、视网膜静脉阻塞、视网膜动脉阻塞、视网膜血管炎症等；视网膜血管瘤病以及其他各种视网膜病所致玻璃体出血；视神经炎、视神经缺血、视网膜脱离、黄斑部疾病如老年性黄斑变性、中浆、中渗等及其他疑难病如葡萄膜炎，青光眼等的诊治积累了大量的临床经验。

Results: Various extent of gyrus-like or banded calcifications were showed in cortex of 8 all cases, cerebral hemisphere atrophy in 4 cases and thickened skull in 3 cases on the diseased side were accompanied. Ocular hemangioma of choroid and choroids plexus enlargement of lateral ventricle were found in one case. The clinical symptoms and signs of correspondence were found.

结果：8例脑颜面血管瘤综合征均有脑皮层不同程度的脑回样或条带状钙化，4例伴病侧大脑萎缩，3例伴病侧颅板增厚，1例合并眼部脉络膜血管瘤和侧脑室脉络丛增大。8例均出现与CT表现相对应的临床症状和体征。

The particular arrangement of veins in the telencephalon permits them to flow in both directions via medullary veins, as seen with certain disorders, such as deep arteriovenous malformations, Sturge-Weber disease, and the developmental venous anomalies[60], possibly explaining the small diameter and unimportance of parenchymal lesions when such a vein is thrombosed.

这种特殊的解剖分布使得端脑内的静脉可以通过脑穿通髓静脉产生双向血流，这一点在脑深部动静脉畸形、Sturge-Weber病/斯特季-韦伯二氏病/脑眼颜面血管瘤病、脑静脉发育异常等疾病中都可观察到，同时也可以解释当这些静脉受累形成血栓时常产生较小的、甚至不容易被发现的病灶。

According to the clear water experiment, aeration performance of the new equipment is good with high total oxygen transfer coefficient and oxygen utilization ratio.

曝气设备的动力效率在叶轮转速为120rpm～150rpm时取得最大值，此时氧利用率和充氧能力也具有较高值。

The environmental stability of that world - including its crushing pressures and icy darkness - means that some of its most famous inhabitants have survived for eons as evolutionary throwbacks, their bodies undergoing little change.

稳定的海底环境─包括能把人压扁的压力和冰冷的黑暗─意谓海底某些最知名的栖居生物已以演化返祖的样态活了万世，形体几无变化。