脑病

Cerebrotendinous xanthomatosis is a rare autosomal recessive disorder of bile acid synthesis, caused by impaired hydroxylation of cholesterol side chains due to deficiency of the mitochondrial enzyme sterol 27-hydroxylase （CYP27A1）, leading to accumulation of cholestanol and cholesterol in brain and other tissues.

文章摘要：脑腱黄瘤病是一种罕见的常染色体隐性遗传性胆汁酸合成障碍，由线粒体酶固醇27-羟化酶（CYP27A1）缺陷所致胆固醇侧链羟化受损引起，从而导致胆固烷醇和胆固醇在脑和其他组织贮积。

With improved control of blood pressure, many centers have found this entity to be declining in incidence, with hemorrhage due to amyloid angiopathy now seen more commonly.

但随着控制血压技术的逐渐提高，许多医疗中心已发现因为这一因素引发脑出血的几率正在降低，而淀粉样血管病的引发的脑出血却日见常见。

Objective To study the changes of expression of α-SM-actin in some cerebral arterioles with different severities of Aβ deposit in the cases of cerebral amyloid angiopathy.

目的 脑淀粉样血管病患者不同病变程度脑小动脉中α-平滑肌肌动蛋白表迭变化的对比。

Results: There are 10 cases with brain aneurysm, 2 cases with arteriovenous malformation, 4 cases with brain tumors, 2 cases cranial nerve tumour.

结果：18例病人中10例脑动脉瘤，2例动静脉畸形，4例脑肿瘤，2例颅神经肿瘤。

Methods The contusive and lacerated brain tissues 3 to 9 hours after TBI were collected, and the expressions of NGF protein of the aged group (≥ 60 years old) and young group (19 to 59 years old) were analyzed by immunohistochemistry and digital image analysis system, to determine the possible susceptibility differences in the expression of NGF protein between the two groups.

收集重型颅脑损伤开颅手术中的脑挫裂伤组织，应用免疫组化和医学数码图像分析技术，观察老年组（≥60岁）和青壮年组（19～59岁）病人脑损伤后3～9 h 脑挫裂伤组织NGF蛋白的表达差异。

Results The negative correlations were found on the Glasgow Outcome Scoreto the items such as conscious state at admission,Glasgow Coma Score,psychiatric symptoms,hemiplegia,Babinski sign,abnomal degree of Electroencephalogram,focal lesions found by neuro-image investigation and mean peak flow velocityand pulsatility indexof basilar artery and vertebral arteries by transcranial Doppler ultrasonography investigation;The non-correlation was found on the Glasgow Outcome Score to theitems such as headache,febrile,epilepˉsia style,the involvement of cranial nerve,dystaxia,neck stiffness,Cerebrospinal fluid investigation and blood serum enzymology.

结果 入院时的意识状态、GCS、精神症状、偏瘫和/或偏身感觉障碍、巴彬斯基征以及脑电图异常程度、影像学所见的病灶范围、基底动脉和椎动脉的平均峰流速、脉动指数和Glasgow预后评分呈负相关；头痛、发热、癫痫类型、颅神经受累情况、共济运动、脑膜刺激征、脑脊液检查（含压力、蛋白定量、细胞数、HSV-PCR）以及血清酶学的变化和Glasgow预后评分之间无相关性。结论入院时的意识状态、GCS、精神症状、局灶性神经系统体征以及脑电图异常程度、影像学所见的病灶范围、后循环的血管痉挛程度和血流阻力等是影响病脑预后的主要因素。

Results The negative correlations were found on the Glasgow Outcome Scoreto the items such as conscious state at admission,Glasgow Coma Score,psychiatric symptoms,hemiplegia,Babinski sign,abnomal degree of Electroencephalogram,focal lesions found by neuro-image investigation and mean peak flow velocityand pulsatility indexof basilar artery and vertebral arteries by transcranial Doppler ultrasonography investigation;The non-correlation was found on the Glasgow Outcome Score to theitems such as headache,febrile,epilepˉsia style,the involvement of cranial nerve,dystaxia,neck stiffness,Cerebrospinal fluid investigation and blood serum enzymology.

结果 入院时的意识状态、GCS、精神症状、偏瘫和/或偏身感觉障碍、巴彬斯基征以及脑电图异常程度、影像学所见的病灶范围、基底动脉和椎动脉的平均峰流速、脉动指数与Glasgow预后评分呈负相关；头痛、发热、癫痫类型、颅神经受累情况、共济运动、脑膜刺激征、脑脊液检查（含压力、蛋白定量、细胞数、HSV-PCR）以及血清酶学的变化与Glasgow预后评分之间无相关性。结论入院时的意识状态、GCS、精神症状、局灶性神经系统体征以及脑电图异常程度、影像学所见的病灶范围、后循环的血管痉挛程度和血流阻力等是影响病脑预后的主要因素。

Hemiparalysis,one of the present symptoms of apoplexy,makes the patients no self-care,which brings great burden to family and society.

脑的可塑性是运动等各种脑功能恢复的重要机制，是目前中风病临床治疗和基础研究的热点。

Results:There is no obvious difference m FA values of uninjured internal capsule of cerebrum between case group and normal group;the normal group FA values is obviously better than case group;the FA values in hemiparalysis patient\'s impairment encephalic region is much lower than the uninjured side;please refer to the text for the results of fMRI,DTI and focus of disease three-dimensional reconstruction and image fusion.

偏瘫患者病损脑区与健侧脑区相比FA值显著降低。(2)fMRI、DTI以及病灶的三维重建与图像融合结果请参见正文图示。

It consistently concerns fronts of medical techniques and has formed its own advantages and specialties which are at advanced levels in China: integrated use of blood purification, nutrient metabolic support, life-support machine for serious patients; sub hypothermia treatment of acute brain contusion, treatment of hydrocephaly and brain stroke, operation treatment of defect of skull;athletic injury, replacement of bone joints, Spinal Surgery;vessel surgery; minimally invasive operation for larynx, diagnosis and cure of facial nerve paralysis;minimally invasive operation for women patients; treatment of neonatal diseases, and child asthma.

医院始终瞄准医学技术发展前沿，逐步形成了自己的技术优势和专业特色。其中血液净化、营养代谢支持、呼吸机治疗在危重病中的联合应用；急性脑挫伤的亚低温治疗、脑积水与脑卒中的治疗、颅骨缺损的手术治疗；运动创伤、骨关节置换、脊柱外科；血管外科；喉微创手术、面神经麻痹的诊断与治疗；妇科微创手术；新生儿疾病的诊治、儿童哮喘的规范治疗等处于国内先进水平。

According to the clear water experiment, aeration performance of the new equipment is good with high total oxygen transfer coefficient and oxygen utilization ratio.

曝气设备的动力效率在叶轮转速为120rpm～150rpm时取得最大值，此时氧利用率和充氧能力也具有较高值。

The environmental stability of that world - including its crushing pressures and icy darkness - means that some of its most famous inhabitants have survived for eons as evolutionary throwbacks, their bodies undergoing little change.

稳定的海底环境─包括能把人压扁的压力和冰冷的黑暗─意谓海底某些最知名的栖居生物已以演化返祖的样态活了万世，形体几无变化。