胆汁的

Cerebrotendinous xanthomatosis is a rare autosomal recessive disorder of bile acid synthesis, caused by impaired hydroxylation of cholesterol side chains due to deficiency of the mitochondrial enzyme sterol 27-hydroxylase （CYP27A1）, leading to accumulation of cholestanol and cholesterol in brain and other tissues.

文章摘要：脑腱黄瘤病是一种罕见的常染色体隐性遗传性胆汁酸合成障碍，由线粒体酶固醇27-羟化酶（CYP27A1）缺陷所致胆固醇侧链羟化受损引起，从而导致胆固烷醇和胆固醇在脑和其他组织贮积。

There are also many pediatric liver disease, including biliary atresia, alpha-1 antitrypsin deficiency, alagille syndrome, and progressive familial intrahepatic cholestasis, to name but a few.

还有许多儿童肝脏疾病，包括胆道闭锁、阿尔法-1抗缺失，郁积综合症家族性肝内胆汁和进步，是名副其实的。

These canalicular membranes have specialized functions related to bile secretion.

这些管状膜有与胆汁分泌有关的特殊功能。

Results Both differences of Level and Max before and after treatment in two groups were significant (P.01). Conclusion Ultrasonography histogram display can be used to assess dynamically the cholagogic effect in cholelithiasis.

采用B超直方图进行胆囊内胆汁透声度定量测定，能动态地观察胆囊结石、慢性胆囊炎患者利胆治疗的效果。

The optimum condition was determined via orthogonal experiments, and the result shows that the technology of bile extraction and purification adopts 10L chromato bar with 3L bile, gel silica as fixed phase, the mixed chloroform and isopropanol as mobile phase, gradient elution with mobile phase (the mobile phase ratio in extraction of cholalic acid and glycocholic acid is 4:1 , and then becomes 3:2 in extraction of glycocholic acid and glycocholic acid), and eluting velocity of 3～5mL/s .

采用正交试验筛选了柱层析最佳条件，以容积为10L的层析柱进行分离纯化，固定相为硅胶，流动相为氯仿和正丁醇混合溶剂，一次装样量3000mL胆汁，流动相采用梯度洗脱，先按4：1比例分离胆酸和甘氨胆酸，然后按3：2比例分离甘氨胆酸和牛磺胆酸，流动相洗脱速度为3～5mL/s。

Objective It explored the carcino-embryonic antigenvalues of cholecystic bile to diagnose hepatic metastasis of the colonic cancer and to estimate its clinical significance.

目的 探讨胆囊胆汁癌胚抗原值诊断大肠癌肝转移的临床价值。

In the second operation, the cases receiving choleeystostomy had less peritoneal adhesion, anatomic structure changes, haemorrhage[(30-50) mL vs (100-200) mL] and operation time[(2.5-3.0) h vs (3.5-5.0) h] than those receiving choledochotomy with T-tube drainage ,and did not appear inadequate drainage for cystic duet obstruction.

而Ⅰ期行胆囊造瘘术的患儿，未发现有因胆囊管梗阻而致胆汁引流不畅者，且Ⅱ期手术时胆总管周围结构较清晰，手术操作相对容易、出血少(30~50mL)、耗时短(2.5~3.0h)。

These results suggest that choleic acids stasisi is one of the factors of multiple organ damage in obstructive jaundice.

提示胆汁酸滞留是造成阻塞性黄疸全身性损害的因素之一。

The levels of cholic acids are the main alteration in bile acids of the maternal serum.

ICP孕妇血清胆汁酸的组份中，以胆酸水平增高为主。

Two clinical phenotypes for citrin deficiency have been reported. One is adult-onset citrullinemia type II (CTLN2) and another is neonatal intrahepatic cholestasis caused by citrin deficiency.

Citrin缺陷病(citrin deficiency， CD)已报道两种临床表现型，一种是成人发病瓜氨酸血症Ⅱ型(CTLN2)，另一种是citrin缺陷导致的新生儿肝内胆汁淤积症。

With Death guitarist Schuldiner adopting vocal duties, the band made a major impact on the scene.

随着死亡的吉他手Schuldiner接受主唱的职务，乐队在现实中树立了重要的影响。

But he could still end up breakfasting on Swiss-government issue muesli because all six are accused of nicking around 45 million pounds they should have paid to FIFA.

不过他最后仍有可能沦为瑞士政府&议事餐桌&上的一道早餐，因为这所有六个人都被指控把本应支付给国际足联的大约4500万英镑骗了个精光。