等比

Gene mutations were detected in 25 patients and a 18-year-old girl among 16 families. Trinucleotide repeats of CAG were 73～79. The fragments of abnormal alleles were 380～402bp, and all patients were heterozygous. The copy numbers of normal alleles were 18～40, fragments from 202～270bp. SCV reduction was much obvious compared to MCV, MCV and SCV in lower limb ?ere much more slow than that in upper's. BAEP, VEP were also delayed in latency. The anticipation in parental sex bias were much more obvioius than that in matental's. Cerebellar ataxia was most severe, the next were dysarthria and bulging eyes. Amytrophy was seen only in bed ridden patients. Cerebellar atrophy was more severe than brain stem, cord atrophy was n't observed in all MJD.

结果检出10个家系25例病人及1例症状前18岁女孩有MJD基因突变，CAG三核苷酸重复73～79次，异常等位基因片段长380～402bp，均为杂合子；正常人CAG三核苷酸重复18～40次，等位片段长200～270bp，电生理发现MJD的SCV减慢比MCV明显，而下肢的MCV、SCV又较上肢明显，BAEP、VEP均有不同程度的潜伏期延长或波的异常；MJD的父亲遗传早于母亲，进展也较块，临床以小脑性共济失调为突出症状，其次为构音障碍、突眼等，肌肉萎缩仅见于晚期病人；MRI示小脑萎缩较明显，脑干萎缩并不严重，未见明显的颈髓萎缩。

Based on KT-01 nickel catalyst, the scientific research personnel of our company and the expert group of the former subject group from Lanzhou University made joint efforts to tackle the key problems and successfully developed the 2nd generation of KT-02 supported nickel catalyst through in-depth study on the technical formula, catalytic activity and other mechanisms and taking modified carrier, the properties of acid and alkali, the degree of decentralization of active ingredients on the carrier surface, and fundamental breakthrough has been achieved on the aspects of catalytic activity, specific surface area, bulk density, etc, and the technical defects of KT-01 nickel catalyst are completely overcome; the catalytic activity becomes higher, the starting temperature becomes lower, the industrial serviceability temperature is lowered and the yield increased.

在KT-01型镍催化剂的基础上，我公司科研人员与兰州大学原课题组专家联合攻关，通过对工艺配方及催化活性等机理的深入研究，从载体改性、酸碱性、活性组分在载体表面的分散程度等方面入手，成功开发出第二代KT-02负载型镍催化剂系列产品，在催化活性、比表面积和堆密度等方面都有根本性突破，彻底克服了KT-01型镍催化剂的技术缺陷，使催化活性更高、启动温度更低，降低了工业使用温度，提高了生产收率。

The study has shown:(1) With increasing sediment depth and the woody giblets, the total organic carbon, the extraction of benzene , the total humic acids and the unhydrolyte are enhanced, while the hydrolyte is decreasing.(2) According to the GC-MS analysis, n-alkane,n-alkan-2-ones and n-alkanones are composed mainly of long-chains,such a result is thought to be characteristic of a herbaceous input from 2300a.B.P. n-alkanones exist in the samples may be considered as the evidence of microorganisms activity.(3) It is showed that the lipids is more sensitive to the climate change than the floristic. The proxy of the pollen spore of the peat stratum is different from the normal environment proxy. It is one of the main reasons that the sensitivity difference of the bog vegetation reacting to the climate isn't accordant with the log of the fat molecule fossil and biology fossil.(4) The transformation of the peat organic carbon is under the influence of temperature,acidity,organic material constituting, etc, and it showed the up-trend with the depth. In the short-term scale, the conversion of the peat organic carbon is effected by seasonal water,regional climate and vegetations; while in the long-term scale, it is controlled mainly by the climate.(5) According to the comparing the orderliness of organic compound,vegetation giblets with the depth to the characteristics of the peat molecule fossil with the section, in the development of this peatmire, 1500a B.P（210cm）is regard as the borderline of the late Holocene, the keynote of the front period is warm with several cold fluctuations, and the trend of the back period is dry and cold although there were several fluctuations.

研究表明：（1）随深度的增高及植物残体中木本残体的增多，总有机碳、苯萃取物、总腐植酸、不被水解物含量逐渐增高，而易水解物含量减少；（2）GC- MS分析显示，正构烷烃，直链烷基2-酮和正烷醇均以长链组分为主，揭示了该泥炭柱剖面2347a.B.P的母源输入以草本植物为主；甲基酮类和短链正烷醇的存在是微生物活性很大的生物证据；（3）通过有机分子标志物与孢粉、植物残体等指标的对比研究表明：脂类化合物对气候变化的反映要比植物种灵敏得多，不同沼泽植物对气候变化的敏感性的差异是脂类分子化石记录与生物大化石结果很难一致的主要原因之一；（4）泥炭有机碳的转化受到温度、酸度、有机物质组成等很多因素的影响，短时间尺度，泥炭有机碳的转化受季节性降水、地方气候和植被等因素的影响；长时间尺度，泥炭地有机碳的转化，受气候条件控制；（5）总结泥炭分子化石特征、泥炭有机质各组分含量及植物残体组成随深度的变异规律，分析结果显示该泥炭地层形成过程中，1500a B.P（210cm）可作为划分前后晚全新世的界线，前期的基调是气候偏暖，但又有几次偏干冷气候的反复，后期气候以干冷为主，其间虽有几次上升波动，但整体趋势不变。

In white participants, the 1919T allele was associated with increased risk of stroke and cardioascular mortality, and in black participants, homozygosity for the 790T allele was associated with a fourfold increased risk of MI compared with homozygosity for the 790A allele.

在白人参与者中，1919T等位基因与中风和心血管病死亡率的危险增加有关，而在黑人参与者中，790T等位基因的同合子性比790A等位基因的同合子性与心肌梗死危险的关系高四倍。

Damsite selection of Yilan Navigation Hydro- junction on Songhuajiang River;2. Study on the general layout scheme for reinforcement and extension project of Guoyang junction sluice;3. The river reach of Dadingzishan Navigation-power junction engineering is characterized by wide grade II terrace,large distance between the two dikes,thick covering of river bed,and strong movability and permeability of riverbed,and the overall layout is the essence of construction of low-head navigation-power junction on the reach.

松花江大顶子山航电枢纽工程河段具有Ⅱ级台地宽、两岸堤距大、河床覆盖层厚、河床质可动性及渗透性强等特点，该河段兴建低水头航电枢纽工程其总体布置是关键，利用正态物理模型(11∶00)及遥控自航船模等研究手段，对大顶子山航电枢纽工程预可、工可、初步设计及施工图设计等阶段枢纽总体布置进行了多方案比选，提出枢纽主要建筑物布置：自右岸依次为船闸、10孔泄水闸、电站、28孔泄水闸及土坝。

DZP-250F/400F type multi-function fully automatic lower feeding film speed pillow-shaped packaging machine, which is mainly applied to the packaging of biscuit, betel nut, snowy ice-lolly, yolk pie, instant noodles, chocolate, candy, western snacks, tableware for aerial food, transparent soap, hotel articles, wet towel, gauze mask, IC card, cartoon card, electric components, trademark, little hardware etc. it has the function of anti-moisture, dustproof and photonegative, and also enhances the product level and additional value. It can save more than 20% cost than using the manual packaging, and it can combine the aluminum plastic packaging macnine and thermalcontraction packaging machine to manufacture.

概述：DZP-250F/400F型全自动下走膜枕式包装机采用下走膜包装，主要适用于食品、日化、化妆品、五金、电子等行业的饼干、槟榔、雪饼、雪糕、蛋黄派、方便面、巧克力、糖果、西点、航空食品、一次性餐具、透明皂、宾馆用品、湿巾、口罩、IC卡、卡片、卡通卡、电器元件、商标、小五金等块状物品的包装，起到防潮、防尘、避光的作用，同时提高了产品档次和附加值，使用该机比手工制袋包装节约成本20%以上，而且可与铝塑包装机、热收缩包装机等机械联运生产。

Considering steel slags ingredients of C_3S, C_2S, f-CaO and Ca_2, liquid A was produced with steel slag combined with salic materials such fly ash, slag or metakaolin as a substitution for cement, based on which, a high performance sodium-silicate suspension two-shot grouting material was developed with characteristics of its excellent workability, strengthening capacity, durability, cost-effectivess, energy-conserving and environmental friendliness.

根据钢渣含C_3S、C_2S、f-CaO和Ca_2等组成的特点，提出以钢渣复合粉煤灰、矿渣或偏高岭土等硅铝质材料取代水泥形成低水灰比A液，开发出一种新型的高性能水玻璃悬浊型双液灌浆材料，该材料具有良好的工作性能、高固结性能、高耐久性能、节能和环保、高性价比等特点。

Based on the analysis of this study, the major counseling and guidance principles are establishing and maintaining good relationship between teacher and student, accepting and advising children, fairness, teacher's words conforming with higher actions, and other counselling viewpoints; the essential principles of adaptation include a positive attitude toward reality, self-directing and hard working, proper combination of toughness and gentleness, survival in distress, and other viewpoints relative to the adaptation of oneself to the external environment; and leadership principles include using normative power, contingency, and the important characteristics associated with leaders.

主要之辅导原理为包容接纳儿童、辅导儿童自导、建立良好的师生关系、至诚、渐进、豫防、境教身教言教并重、动静相济、公平无私、日新其德、变通、仁合於义、与时偕行、只管耕耘不计收获、周而能异、遏恶扬善、益之用凶事、以果行首德、爱而严之教育态度、恒久於其道而天下化成、有德长老之领导、熟练以致用、不可急速正其不正等；主要之适应原理为中且正、亲比、天下随时、包含章美、积极面对现实、敬慎、努力充实自己、自强不息、自我尝试、自求、刚而能柔、柔而能刚、积种倾倒否塞、艰难以处之、内健而外顺、生於忧患、反身修德、利人、至诚、安而不忘危、见几而作等；主要之统御原理为在莅众用晦而明、师出以律、无为、以孚信化邦、以贵下贱、知临、咸感以临下、威临吉无不利未顺命也、变而过之以尽利、在师中吉、劳谦、敬之无咎、长子帅师、容民畜众、君子央央、师或舆尸凶、师左次无咎、慎密、匪其彭无咎、有孚维心亨、作事谋始、圣人感人心、明慎用那而不留狱、先甲三日后甲三日、致命遂志、涣其躬、涣其羣、动而免乎险、上以厚下安宅、思不出其位等。

Experts, the expansion of the chemical agent called motilin cells, hormones are chemical substances, commonly used fruits and vegetables have a kiwi, watermelon, strawberries, cherries, tomatoes, and some vegetable farmers in the cucumber, summer squash and other vegetables used in this way to make fruits and vegetables-cell non-normal enlargement, head of fruits and vegetables grown up than the normal 1-2 times as large, the shape become more exotic, such as tomatoes, long tip, strawberries were piriform, cucumber apex hypertrophy with pedicle sharp contrast and so on.

专家介绍，膨大剂的化学名称叫细胞集动素，属于激素类化学物质，常用的果蔬有猕猴桃、西瓜、草莓、樱桃、西红柿等，有些菜农在黄瓜、西葫芦等蔬菜上使用，以此方法使果蔬细胞非正常膨大，个头比正常长大的果蔬大1—2倍，形状变得比较奇特，如西红柿长尖、草莓呈梨状，黄瓜尖部肥大与蒂部形成鲜明对比等。

4The electrical double layer model, joining with the microstructure of CFRC,fractal electrical emission, electrothermal effect, thermoelectrical effect and electrical osmosis are used to analyze the mechanism of mechanoelectric effect and electromechanical effect of CFRC.

采用正交试验方法研究了不同配比分散剂对碳纤维在水泥基体中分散性的影响，得到了较佳分散剂配比，探讨了分散剂的作用机理和碳纤维长度分布规律；（2）研究了碳纤维水泥基复合材料中纤维掺量、水灰比、电极形式、载荷形式等对力电效应的影响，考察了CFRC力电效应的两种表现形式及在机敏混凝土结构上的应用；（3）研究了CFRC立方试块、CFRC梁和不含导电填料梁的电力效应，分析了电流大小、电流方向等与电致变形的关系；（4）根据界面电偶层模型，结合CFRC的微观结构，以及断裂电发射、电热效应、热电效应和电渗效应等分析了CFRC力电、电力效应的机理，阐明碳纤维的作用机制。

According to the clear water experiment, aeration performance of the new equipment is good with high total oxygen transfer coefficient and oxygen utilization ratio.

曝气设备的动力效率在叶轮转速为120rpm～150rpm时取得最大值，此时氧利用率和充氧能力也具有较高值。

The environmental stability of that world - including its crushing pressures and icy darkness - means that some of its most famous inhabitants have survived for eons as evolutionary throwbacks, their bodies undergoing little change.

稳定的海底环境─包括能把人压扁的压力和冰冷的黑暗─意谓海底某些最知名的栖居生物已以演化返祖的样态活了万世，形体几无变化。