强直

Another feature of this syndrome is delayed muscle relaxation, which differs from true myotonia by absent percussion myotonia and increased rather than decreased stiffness during continued activity.

Isaacs综合征的另一个特点是肌肉松弛延缓。1。 Isaacs综合征患者，无叩击性肌强直；2。持续活动期间，肌强直加剧而非减轻。

Current neurological examination disclosed percussion myotonia and myotonia as and DNA analysis. The patient's mother, though minimally affected, had similar laboratory results.

神经学检查，发现有肌强直现象，并由典型的肌电图变化及脱氧核醣核酸分析，确定为先天型肌强直失养症的此病。

Previous studies indicate that several mutations alter the voltage dependence of hClC-1 channels. Besides changing the gating property of the Cl- channel, other defects in mutant hClC1 channels may also contribute to the mechanism of myotonia congenita.

前人的研究指出一些与先天性肌肉强直症相关的突变会改变hClC-1通道的电位依赖性，然而除了藉由影响离子通道的门阀开关比例之外，其他由於基因突变造成hClC-1通道的缺失也可能为先天性肌肉强直症的致病机转的成因。

DM1 and DM2 gene were amplified by PCR,tested by agarose electrophoresis, then analyzed by genetic analyzer. Results: Myotonia and muscle weakness were the main manifestations associated with heart block (7/8) and cataract (6/7). Electromyologram showed myopathic abnormalities not only in patients but also in other members of the family (5/6). The CTG repeats in DM1 and CCTG repeats in DM2 were all in normal range.

结果：该家系患者除有肌强直、肌萎缩等表现外；心电图检查：心脏传导阻滞(7/8)；裂隙灯检查：白内障(6/7)；肌电图检查：患者组有强直电位发放(5/5)，无临床症状成员也存在肌源性损害(5/6)；但该家系无DM1位点n和DM2位点n的重复数增加。

In the present study, the effects of 2 Hz and 100 Hz tetanic parameters on L-LTP of the field potentials were recorded from the layer Ⅱ/Ⅲ of the rat visual cortical slices in response to stimulation of the layer Ⅳ.

本研究用3周龄的大鼠视皮层脑片标本，在Ⅳ层刺激而在Ⅱ/Ⅲ层记录场电位，待场电位稳定后施加强直刺激诱导LTP，探讨2Hz与100Hz的强直刺激在诱发持续时间长于3h的L-LTP中的作用。

With prolonged lowfrequency tetanization, a temporary inhibitory change was often observed immediately after the tetanic stimulation. But the evoked potentials began to recover more than ten minute later and finally exceeded the pre-tetanic level.

在较长的低频强直刺激下，往往先引出一抑制性变化，但十几分钟后反应逐渐恢复并将超过强直刺激前水平。

The straight gneisses have the plane-straight gneissic; beating a few, fine and plane-straight felsic streaks; the mineral stretching lineation; as the S-L tectonite with the features of finer mineral grain size (1mm±), uniform grain size grade and bad directional, showing the ultra-plastic flow mechanism.

强直片麻岩发育平直的片麻理，长英质条带含量相对较低，但细而平直，发育矿物拉伸线理，为S-L构造岩，矿物粒度相对较细(1mm±)，粒级均匀，定向性差，均反映出强直片麻岩的超塑性流动变形机制特征。

The decoction relieved muscle rigidity more effectively than tremor.It could improve hypokinesia and quality of life fundamentally.

补肾活血饮对强直明显者疗效较震颤者显著，说明其能明显缓解肌强直，从根本上改善患者的运动功能和日常生活能力。

AIM To investigate the surgical treatments on ankylosed hip joints with flexion informity, 11 cases of total hip arthroplasty course and postoperative treatment were analysed retrospectively.

目的 通过回顾性分析髋关节屈曲强直后的治疗经过，对髋关节屈曲强直后的人工全髋关节置换术的外科治疗方法进行探讨。

Quick movements cause muscle stiffen ing. There is also a myotonic form of muscular dystrophy.

快速运动会引起肌强直，肌营养不良是另一种肌强直类型。

According to the clear water experiment, aeration performance of the new equipment is good with high total oxygen transfer coefficient and oxygen utilization ratio.

曝气设备的动力效率在叶轮转速为120rpm～150rpm时取得最大值，此时氧利用率和充氧能力也具有较高值。

The environmental stability of that world - including its crushing pressures and icy darkness - means that some of its most famous inhabitants have survived for eons as evolutionary throwbacks, their bodies undergoing little change.

稳定的海底环境─包括能把人压扁的压力和冰冷的黑暗─意谓海底某些最知名的栖居生物已以演化返祖的样态活了万世，形体几无变化。