查询词典 epidermolysis

I have finally learned how to say, that I have a rare orphan genetic skin disorder named recessive dystrophic epidermolysis bullosa.

现在我终于学会解释自己的病了：这是一种罕见的遗传性皮肤病，叫隐性遗传营养不良型大疱性表皮松解症。

Methods 10 cases of anti-P_(200) pemphigoid sera were collected. The skin sections from 6 cases of recessive dystrophic epidermolysis bullosa were studied with these sera by indirect immunofluorescence.

方法收集了10例抗P_(200)类天疱疮血清，对6例隐性遗传性营养不良性大疱性表皮松解症皮肤切片进行了间接免疫荧光研究。

Dystrophic epidermolysis bullosa is a group of genetic disease caused by loss-of-function mutations in the type Ⅶ collagen gene. The clinical phenotype is characterized by the blistering and scaring of the skin from trauma and there is increased complication of squamous cell carcinoma, which is the major cause of death in patients with DEB.

营养不良性大疱性表皮松解症是一种由于人体Ⅶ型胶原基因突变或缺失所引起的遗传性疾病，临床特征为创伤诱发的水疱和瘢痕，并发症以恶性鳞状细胞癌多见，是导致患者死亡的主要因素，目前仍无有效的治疗方法。

Here, we report on the first systematic long-term study of fibroblast therapy in a mouse model for recessive dystrophic epidermolysis bullosa, a severe skin-blistering disorder caused by loss-of-function of collagen VII.

我们报道了第一例长期性系统性的关于成纤维细胞治疗隐性营养不良性大疱性表皮松解症小鼠模型的研究。隐性营养不良性大疱性表皮松解症是一种严重的由于VII-胶原蛋白功能丧失引起的出疱性皮肤病。

Results All the 10 anti-P_(200) pemphigoid sera could react with basement membrane zoneof 5 cases of recessive dystrophic epidermolysis bullosa, while epidermolysis bullosa acquisita sera were negative in these skins.

结果发现10例抗P_(200)类天疱疮血清均与5例RDEB皮肤基底膜带反应，而获得性大疱表皮松解症血清对这些皮肤为阴性。

Epidermolysis bullosa is the name given to a group of genetic disorders that lead to fragile skin.

大疱性表皮松解症的名称是给一组遗传性疾病导致脆弱的皮肤。

Preclinical progress has been achieved in the treatment of wounds, epidermolysis bullosa and ichthyosis.

前期的临床实验在治疗创伤，大疱性表皮松解症和鱼鳞病上已经取得了进展。

Objective To study the gene mutation in a pedigree with Dowling-Meara type epidermolysis bullosa simplex .

目的研究Dowling-Meara亚型单纯型大疱性表皮松解症一家系的基因突变。

It has been demonstrated that Laminin 5 is close related to skin tissue engineering, genesis and metastasis of rumour ,and inherited junctional epidermolysis bullosa.

该蛋白已被证实与皮肤组织工程、肿瘤的迁徙、及遗传性大疱性表皮松懈症(iunctional epidermolysis bullosa，JEB)有密切的关联。

In addition,in a case of recessive dystrophic epidermolysis bullosa, epidermolysis bullosa acquisita sera react with both BMZ and intracytoplasmic deposition of type Ⅶ collagen,while no anti-P_(200) pemphigoid sera showed this reactivi- ty.

另外，在1例RDEB，EBA血清既与BMZ反应又与Ⅶ型胶原沉积部位的胞浆反应，而抗P_(200)类天疱疮血清无此反应。

Lugalbanda was a god and shepherd king of Uruk where he was worshipped for over a thousand years.

Lugalbanda 是神和被崇拜了一千年多 Uruk古埃及喜克索王朝国王。

I am coming just now,' and went on perfuming himself with Hunut, then he came and sat.

我来只是现在，'歼灭战perfuming自己与胡努特，那麼，他来到和SAT 。