查询词典 amyloidosis

Objective To analyze the clinical characteristics of patients with cardiac amyloidosis.

目的 探讨心脏淀粉样变性的临床特点。

Methods Clinical features of 25 patients with primary systemic amyloidosis admitted to our hospital since 1991 were retrospectively analyzed.

回顾性分析了本院1991年以来收治的25例原发性系统性淀粉样变性患者的临床特征。

Amyloidosis is a relatively rare disease in clinical practice. However, pulmonary involvement in patients with amyloidosis is common.

类淀粉沈积症在临床上被视为一种相对罕见的疾病，然而它对肺部的影响却是很常见的。

Objective To investigate the histopathological findings of primary cutaneous lichenoid amyloidosis and macular amyloidosis.

目的 总结和比较苔藓样型和斑状型原发性皮肤淀粉样变的组织病理学特点。

Amyloidosis cutis dyschromica is a rare distinct type of primary cutaneous amyloidosis characterized by the presence of widespread hypopigmented as well as hyperpigmented macules. We herein report a 25-year-old male showing diffuse hyperpigmentation as with hypopigmented spots over his whole body but sparing his lace, hands and feet from the age of 8 years.

色素异常性皮肤淀粉样变性症是原发性皮肤淀粉样变性症的一个罕见而独特的亚型，其特徵是在皮肤出现广泛的色素沉著及色素脱失的斑点；我们在此报告一位25岁男性自八岁起在全身皮肤出现广泛的色素沉著及色素脱失约斑点，病灶并未侵犯其脸部、手掌、及脚掌。

In patients with biopsy-proven cardiac amyloidosis, late gadolinium enhancement frequently occurs in a peculiar pattern. On the basis of the gold standard, EMB, noninvasive CMRI can be used to diagnose or rule out cardiac amyloidosis with good sensitivity and excellent specificity in a clinical routine setting.

在心肌活检证实为淀粉样变性的患者中，钆延迟增强扫描常常会以特异的方式出现，在此金标准基础上，EMB和非侵入性CMRI可用于诊断或排除心肌淀粉样变性，仅有较高的敏感性和优越的特异性。

Results Stenosis or occlusion of bronchotracheal tree were observed in 5 patients with localized amyloidosis; Among 4 patients with systemic amyloidosis, 3 cases of pulmonary interstitial involvement, 4 cases of pleural thickening, 4 cases of pleural effusion, 3 cases of interventricular septum and ventricular walls thickening , 1 case of pericardial effusion were observed.

结果 5例局限性病变患者均有气管支气管树的狭窄或闭塞，其中2例分别合并左舌叶与右上叶阻塞性肺不张；4例全身性病变患者中肺间质病变3例，胸膜增厚4例，胸腔积液4例，室间隔与左心室肌增厚3例，心包积液1例。

Amylin plays a critical role in islet amyloidosis and in the deelopment of β-cell dysfunction in patients with diabetes; howeer, the inolement of amylin in renal amyloidosis has not been studied.

胰淀素在糖尿病患者的胰岛淀粉样变性及β-细胞机能异常过程中起关键作用；然而尚未研究过胰淀素在肾脏淀粉样变性中的作用。

The primary localized amyloidosis of bronchotracheal tree have characteristic radiographic findings, but the primary systemic amyloidosis have no distinctive radiographic findings, the diagnosis relies on pathology.

局限于气管支气管树的原发淀粉样变病具有一定的影像特点，而全身性原发淀粉样变病累及胸部的有关影像学表现缺乏特征性，诊断依靠病理活检。

RESULTS: Cardiac amyloidosis was detected by EMB in 15 of the 33 patients. In patients with biopsy-proven cardiac amyloidosis, CMRI revealed a distinct pattern of late gadolinium enhancement, which was distributed over the entire subendocardial circumference, extending in various degrees into the neighboring myocardium.

结果：33例患者中，15例EMB证实有心肌淀粉样变性，在EMB证实患者中，CMRI显示延迟钆增强的特殊模式，分布于整个心内膜下，不同程度上延伸至邻近心肌。

It has been put forward that there exists single Ball point and double Ball points on the symmetrical connecting-rod curves of equilateral mechanisms.

从鲍尔点的形成原理出发，分析对称连杆曲线上鲍尔点的产生条件，提出等边机构的对称连杆曲线上有单鲍尔点和双鲍尔点。

The factory affiliated to the Group primarily manufactures multiple-purpose pincers, baking kits, knives, scissors, kitchenware, gardening tools and beauty care kits as well as other hardware tools, the annual production value of which reaches US$ 30 million dollars.

集团所属工厂主要生产多用钳、烤具、刀具、剪刀、厨具、花园工具、美容套等五金产品，年生产总值3000万美元，产品价廉物美、选料上乘、质量保证，深受国内外客户的青睐