查询词典 Pompe

Bandt and Pompe (2002) introduced a complexity measure which has aspects of both dyna mical systems and entropy measures.

Bandt and Pompe (2002)介绍了一种关于动力系统和熵测量方面的复杂度测量的方法。

Enzymatic diagnosis of Pompe disease is hampered by the presence of several isoenzymes in whole blood, of which the neutrophil enzyme maltase-glucoamylase is of particular concern due to its low pH optimum.

酶法诊断庞佩病是受到在场的几个同工酶全血，而中性酶麦芽糖-糖化酶是特别关注，由於其低ph最优。

An autosomal recessive genetic condition, Pompe's disease affects 1 in 40,000 individuals.

该试验已经於12月6日线上发表，并预计於2007年1月9日发表於神经学期刊。

The trial included 18 children diagnosed with Pompe's disease at 6 months old or younger who exhibited severe GAA deficiency and cardiomyopathy.

该试验收纳18位被诊断罹患Pompe氏疾病、年龄低於6个月且已经有严重GAA缺乏与心脏病变婴儿。

In addition to offering a viable treatment option for infants, rhGAA therapy may also offer hope to those with adult-onset Pompe's disease, which is also characterized by muscle weakness but progresses more slowly.

除了提供婴儿一个很重要的治疗选择，rhGAA疗法也提供成人发作型Pompe氏疾病患者一线希望，这些病患同样受肌肉无力之苦，但进展地较慢。

In late-onset Pompe disease, most of the symptoms cannot be reversed by treatment.

婴儿型庞贝氏症患者经由酵素补充疗法，可有效延长性命，恢复心脏正常大小，但是大部分患者的运动及呼吸功能无法恢复正常；晚发型庞贝氏症治疗后，其症状之可逆性也很有限。

Background: Pompe disease is due to a deficiency of lysosomal acid alpha glucosidase, and currently an enzyme replacement therapy has been developed.

中文摘要背景：庞贝氏症是一种因为溶小体缺乏酸性醣苷酶无法分解肝醣所引起之疾病。

The biotechnology company Genzyme spent five hundred million dollars developing the drug Myozyme, which is intended for a condition, Pompe disease, that afflicts fewer than ten thousand people worldwide.

生物技术公司健赞投入5亿美元研发了一种治疗庞贝氏症的治疗药Myozyme，这种疾病的患者在全世界不超过1万名。

The medication developed by the Academia Sinica team is the only approved treatment for Pompe's disease available, giving children who originally thought they would never grow up, another chance at life.

全球唯一也是第一个治疗庞贝氏症的药物，核准上市，更奠定治愈其他肌肉病变的基础，这也给了更多原本以为长不大的孩子，一线希望。

We conducted a randomized, placebo-controlled trial of alglucosidase alfa, a recombinant human GAA, for the treatment of late-onset Pompe''s disease.

咱们进行了一项用阿葡糖苷酶α治疗晚发式蓬佩病的RAND、慰藉剂对于照试验。

More direct, directer ; most direct, directest

径直的，笔直的

Do you know how to use a chain saw?

你知道如何使用链锯吗？